Wednesday, October 26, 2011

Ahead of Print: Facial Reanimation of Patients with Neurofibromatosis Type 2

Full article access for Neurosurgery subscribers at Neurosurgery-Online.com.

BACKGROUND: Neurofibromatosis type 2 (NF2) is a tumor suppressor syndrome defined by bilateral vestibular schwannomas. Facial paralysis – either from tumor growth or from surgical intervention – is a devastating complication of this disorder and can contribute to disfigurement and corneal keratopathy. Historically, physicians have not attempted to treat facial paralysis in these patients.

OBJECTIVE: We review our clinical experience with free gracilis muscle transfer for the purpose of facial reanimation in patients with NF2.

METHODS: Five patients with NF2 and complete unilateral facial paralysis were referred to the facial nerve center at our institution. Charts and operative reports were reviewed; treatment details and functional outcomes are reported.

RESULTS: Patients were treated between 2006 and 2009. 3 patients were men and 2 were women. The age of presentation of debilitating facial paralysis ranged from 13 to 50 years old. All patients were treated with a single stage free gracilis muscle transfer for smile reanimation. Each obturator nerve of the gracilis was coapted to the masseteric branch of the trigeminal nerve. Measurement of oral commissure excursions at rest and with smile, preoperatively and postoperatively, revealed improved and near symmetric smile in all cases.

CONCLUSION: Management of facial paralysis is oftentimes overlooked when defining a care plan for NF2 patients who typically may have multiple brain and spine tumors. The paralyzed smile may be treated successfully with single stage free gracilis muscle transfer in the motivated patient.

Full article access for Neurosurgery subscribers at Neurosurgery-Online.com.







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